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The mutations reported from Protein C are listed below:

Click on the highlighted residues for further information on mutation.


MWQLTSLLLFVATWGISGTPAPLDSVFSSSERAHQVLRIRKRANSFLEELRHSSLERECI
EEICDFEEAKEIFQNVDDTLAFWSKHVDGDQCLVLPLEHPCASLCCGHGTCIDGIGSFSC
DCRSGWEGRFCQREVSFLNCSLDNGGCTHYCLEEVGWRRCSCAPGYKLGDDLLQCHPAVK
FPCGRPWKRMEKKRSHLKRDTEDQEDQVDPRLIDGKMTRRGDSPWQVVLLDSKKKLACGA
VLIHPSWVLTAAHCMDESKKLLVRLGEYDLRRWEKWELDLDIKEVFVHPNYSKSTTDNDI
ALLHLAQPATLSQTIVPICLPDSGLAERELNQAGQETLVTGWGYHSSREKEAKRNRTFVL
NFIKIPVVPHNECSEVMSNMVSENMLCAGILGDRQDACEGDSGGPMVASFHGTWFLVGLV
SWGEGCGLLHNYGVYTKVSRYLDWIHGHIRDKEAPQKSWAP

Missense

Position* Wild type Mutant Domain PMID
43AlaThrGla10669160
44AsnIleGla19133979, 20187890
47LeuGlnGla7701473
48GluGlyGla16360797
49GluAspGla7974343
51ArgCysGla8446940, 7482420, 7670104
51ArgHisGla10691853, 15634335
52HisGlnGla15634335
53SerArgGla10669160
53SerGlyGla10669160
54SerArgGla10669160
54SerAsnGla10669160
54SerCysGla7795150, 10669160
55LeuProGla8972002
57ArgGlnGla7951255, 8889822
57ArgGlyGla8477066
57ArgLeuGla8889822
57ArgProGla8889822
57ArgTrpGla8477066, 8499568, 8446940, 7482420, 7792728, 12439046, 779
58GluAspGla7701473
62GluAlaGla1347706, 7482420
62GluGlnGla7482420
65AspSerGla15634335
68GluAspGla7701473
68GluLysGla8115990
74GlnAlaGla15634335
74GlnGluGla8110790
75AsnAspGla15634335
76ValAlaGla15634335
76ValMetGla7489240, 1347706
77AspAlaGla15634335
77AspGlyGla11091192, 7670104
82PheLeuGla7670104
84MetThrGla7865674
86HisTyrGla15634335
88AspAsnGla16360797
88AspTyrGla18751723
89GlyCys 7605880
90AspGlu 8950780
96ProSer 7981702
106CysGlyEGF-like 116360797
106CysTrpEGF-like 117649704
108HisAsnEGF-like 110942114
108HisAspEGF-like 110942114
110ThrArgEGF-like 110669160
113AspAlaEGF-like 18950780
114GlyArgEGF-like 17792728
114GlyCysEGF-like 116360797
118PheLeuEGF-like 17670104
118PheValEGF-like 110669160
125GlyCysEGF-like 110942953
129ArgHisEGF-like 18845458
131CysSerEGF-like 110669160
133ArgPro 10669160
144AsnIleEGF-like 210669160
144AsnLysEGF-like 27841323
144AsnSerEGF-like 218725346
145GlyArgEGF-like 28292730
147CysTyrEGF-like 221811774
149HisProEGF-like 28292730
166TyrCysEGF-like 28607097
176HisAsnEGF-like 211243145
178AlaPro 7878626, 8208728
181PheLeu 16689777
181PheVal 10810872, 9840027, 10805275, 17649704
185ArgSer 9840027
189ArgTrp 15114590, 8208728
200AspGlu 10669160
209AspGly 8208728
209AspPhe 8208728
210ProLeu 8292730, 8208728
210ProVal 8167337
211ArgGln 12697119, 8208728
211ArgTrp 18376272, 12583631, 17603240, 10810872, 9840027, 10805275,
211ArgTyr 9610620
214AspAsnPeptidase S18208728
215GlyArgPeptidase S116360797
215GlyGluPeptidase S111091192
218ThrIlePeptidase S17705844
220ArgGlnPeptidase S19798967, 7795152, 8807339, 8499565, 1301954, 1301959, 82087
220ArgProPeptidase S17605880
220ArgTrpPeptidase S118799939, 1301954, 16360797
222AspGlyPeptidase S112362235
223SerArgPeptidase S119133979, 20187890
225TrpSerPeptidase S111091192
226GlnHisPeptidase S17974377, 8208728
235LysGlnPeptidase S110669160
243IleThrPeptidase S18292730, 8208728
244HisTyrPeptidase S18208728
248ValAlaPeptidase S115114590
252AsnValPeptidase S19788727
253HisGlnPeptidase S18208728
254CysArgPeptidase S116360797
265LeuPhePeptidase S18208728, 8128429, 15114590
267GluLysPeptidase S17906267
271ArgGlnPeptidase S17974343, 8324221, 8208728
271ArgTrpPeptidase S18208728
272ArgCysPeptidase S111091192
272ArgHisPeptidase S115114590
272ArgLysPeptidase S19990817
277GluLysPeptidase S17540990
279AspGlyPeptidase S110669160
289ProLeuPeptidase S18208728
290AsnIlePeptidase S19788727
294SerAsnPeptidase S17974343, 8324221, 8208728
296ThrIlePeptidase S111091192, 9990817
297AspHisPeptidase S120829681, 20510102, 19923982, 20860169,
298AsnAspPeptidase S18208728
301AlaSerPeptidase S110669160
301AlaThrPeptidase S111434940, 7605880
301AlaValPeptidase S18208728
309AlaThrPeptidase S120829681, 20510102, 19923982, 20860169,
309AlaValPeptidase S17670104
312SerLeuPeptidase S17670104, 11380450
312SerProPeptidase S17670104, 7919373
320LeuArgPeptidase S110669160
321ProLeuPeptidase S18292730, 7831652
324GlyArgPeptidase S17792728
324GlySerPeptidase S17831652
328ArgCysPeptidase S17792728
328ArgHisPeptidase S19840027, 7878626, 8208728
330LeuIlePeptidase S115978566
332GlnHisPeptidase S110669160
334GlySerPeptidase S18208728
335GlnHisPeptidase S17670104
339ValMetPeptidase S110810872, 9840027, 10805275, 8883262, 7670104
340ThrLysPeptidase S17670104
340ThrMetPeptidase S19798967, 7913773, 8292730, 8208728, 7670104
342TrpCysPeptidase S116360797
343GlyAspPeptidase S18208728
348ArgGlnPeptidase S117872949
356ArgHisPeptidase S17670104
367ValAlaPeptidase S116360797
367ValMetPeptidase S116360797
369ProLeuPeptidase S17792728, 7865674
373CysArgPeptidase S19840027
377MetThrPeptidase S17670104
383GluGlyPeptidase S19840027
385MetIlePeptidase S17670104
388AlaGluPeptidase S110669160
388AlaThrPeptidase S19690806, 8208728
388AlaValPeptidase S18208728
389GlyAlaPeptidase S110942114
389GlyAspPeptidase S110669160
392GlyArgPeptidase S17865674
394ArgTrpPeptidase S110691853, 7831652, 8208728
397AlaValPeptidase S19788727
401AspAsnPeptidase S19840027, 7865674, 9990817, 8208728
402SerAlaPeptidase S19007985
406MetIlePeptidase S110810872, 9840027, 10805275, 8165644, 8883262
406MetTrpPeptidase S111091192
410PheSerPeptidase S19840027
412GlySerPeptidase S17670104
414TrpArgPeptidase S110669160
416LeuProPeptidase S110669160
418GlyAspPeptidase S11611081, 8208728
422TrpCysPeptidase S19840027
422TrpGlyPeptidase S114989454, 10942114
423GlyAspPeptidase S18018768
423GlySerPeptidase S18208728, 8018768, 8398832
426CysTyrPeptidase S18292730
429LeuPhePeptidase S19840027
431AsnLysPeptidase S17670104
433GlySerPeptidase S18208728, 15978566
436ThrAspPeptidase S18829639
441TyrHisPeptidase S17865674
444TrpCysPeptidase S12437584, 16113807
445IleLeuPeptidase S17670104
445IleMetPeptidase S18208728, 8128429, 7670104

Insertion

Mutation Codon Exon/Intron Domain PMID
 9-bp insertion    Exon 5    8972002
 8826insCCTG    Exon 9    12695756
 3363insC        9798967
 3350insA        7841323
 insC        7913773, 10805275, 8446940, 2521802
 6139insTT        1301954
 3350insA        7841323
 3363insC        9798967

Deletion

Mutation Codon Exon/Intron Domain PMID
 del Lys150/ 151        12492584, 9840027, 17649704
 7173-7182delGCGGGGCAGT    Exon 8    15748260
 8857delG        10810872, 9840027, 10805275, 1469096, 8883262
 5bp del 3455-3459    Exon 6    7919373
 delCCCGC    Exon 6    1611081
 del  364      8292730
 3447-3451delCCCGC    Exon 6    1611081
 3351del        7841323
 3ntdelAAG    exon7    19822351
 3ntdelGAC    exon9    21744130

Nonsense

Mutation* Codon Exon/Intron Domain PMID
 Cys59X      Gla  18376272
 Trp83X    Exon 4  Gla  11336399
 Cys105X      EGF1  1868249
 Arg157X      EGF2  8499565
 Gln174X    Exon 6  EGF2  8607097
 Gln174X    Exon 6  EGF2  1868249
 Trp187X        8292730
 Arg199X    Exon 7    9990817, 8499565, 1301959, 7894031
 Arg348X      Peptidase S1  1348046, 2437584, 1868249

Polymorphism

Mutation* Codon Exon/Intron Domain PMID
 Cys154Thr        17603240
 Pro21Pro        8972002
 Ser141Ser      EGF2  17603240

Splice site

Mutation Codon Exon/Intron Domain PMID
 G2992A    Intron D    7792728
 G3079A        9840027
 6274C>T    Intron G    1301954
 3318A>G    Intron 5    8244342

* The positions are based on the protein sequence inclusive of the signal peptide if present.


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